Is limited scleroderma the same as CREST?
Some people have a type of scleroderma called CREST syndrome (or limited scleroderma). Unlike other types, which only affect the arms, legs, and face, this kind can involve your digestive tract. While less common, it can also lead to problems with your heart and lungs.
What is the life expectancy of someone with CREST syndrome?
What Is the Life Expectancy for CREST Syndrome? The survival rate for of CREST syndrome (limited scleroderma) from time of diagnosis is estimated to be as follows: 77.9% at 5 years. 55.1% at 10 years. 37.4% at 15 years.
How long can you live with limited scleroderma?
People who have localized scleroderma may live an uninterrupted life with only minor symptom experiences and management. On the other hand, those diagnosed with an advanced and systemic version of the disease have a prognosis of anywhere from three to 15 years.
Is limited scleroderma a rare disease?
Scleroderma is a rare autoimmune connective tissue disorder characterized by abnormal thickening of the skin.
Can you live a normal life with CREST syndrome?
In a large 2003 US study by Mayes et al, the survival rate from time of diagnosis was computed to be 77.9% at 5 years, 55.1% at 10 years, 37.4% at 15 years, and 26.8% at 20 years. The extent of skin involvement is a good predictor of survival in patients with scleroderma.
What are the symptoms of limited scleroderma?
Symptoms
- Tight, hardened skin. In limited scleroderma, skin changes typically affect only the lower arms and legs, including fingers and toes, and sometimes the face and neck.
- Raynaud’s phenomenon.
- Red spots or lines on skin.
- Bumps under the skin.
- Swallowing difficulties.
Is limited scleroderma hereditary?
Genetics plays a role in the disease, but it is not passed on from parents to children, and it’s rare for immediate family members of those with scleroderma to get it. It is common for family members, however, to have other autoimmune diseases such as thyroid disease, rheumatoid arthritis or lupus.
Do I really have limited scleroderma?
With limited scleroderma, the skin changes are typically limited to the fingers and lower arms, toes and lower legs, and the face. With diffuse scleroderma, the changes can cover more of the body including upper arms and legs and the trunk area.
What is the prognosis of CREST syndrome?
The survival rate for of CREST syndrome (limited scleroderma) from time of diagnosis is estimated to be as follows: 77.9% at 5 years. 55.1% at 10 years. 37.4% at 15 years. 26.8% at 20 years. Limited skin disease is associated with a better survival rate than widespread disease.
Is limited scleroderma life threatening?
Limited scleroderma does not cause major problems. It is limited to the skin. It develops gradually and slowly. It becomes life threatening when it involves the lungs or heart. Scleroderma can be mild or severe that can be fatal. It can be life threatening. Its seriousness depends on the involvement of the organ and extent of its affection.
What are the medications for CREST syndrome?
Reduce and remove risk factors and triggers. Stop smoking,avoid beta-blockers,and avoid any remediable underlying cause (eg,use of vibratory equipment).[113]